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DeCS
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Descriptor English:
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Dandy-Walker Syndrome
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Descriptor Spanish:
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Síndrome de Dandy-Walker
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Descriptor Portuguese:
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Síndrome de Dandy-Walker
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Synonyms English:
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Cyst, Dandy-Walker
Cysts, Dandy-Walker
Dandy Walker Complex
Dandy Walker Deformity
Dandy Walker Malformation
Dandy Walker Syndrome
Dandy Walker Syndrome, Familial
Dandy-Walker Complex
Dandy-Walker Complices
Dandy-Walker Cyst
Dandy-Walker Cysts
Dandy-Walker Deformities
Dandy-Walker Deformity
Dandy-Walker Malformation
Dandy-Walker Syndrome, Familial
Familial Dandy-Walker Syndrome
Hydrocephalus, Internal, Dandy-Walker Type
Hydrocephalus, Noncommunicating, Dandy-Walker Type
Luschka Magendie Foramina Atresia
Luschka-Magendie Foramina Atresia
Malformation, Dandy-Walker
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Tree Number:
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C10.228.140.252.300
C10.228.140.602.500
C10.500.205
C16.131.666.205
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Definition English:
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A congenital abnormality of the central nervous system marked by failure of the midline structures of the cerebellum to develop, dilation of the fourth ventricle, and upward displacement of the transverse sinuses, tentorium, and torcula. Clinical features include occipital bossing, progressive head enlargement, bulging of anterior fontanelle, papilledema, ataxia, gait disturbances, nystagmus, and intellectual compromise. (From Menkes, Textbook of Child Neurology, 5th ed, pp294-5) |
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History Note English:
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1991(1970)
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Allowable Qualifiers English:
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Record Number:
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3635
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Unique Identifier:
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D003616
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Occurrence in VHL:
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Similar:
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DeCS
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